Supravalvular mitral membrane svmm parachute mitral valve. Now, eight lesions are considered part of shone syndrome. Shones complex also known as shone s syndrome, disorder, or anomaly is a rare congenital heart disease consisting of multiple left heart obstructive defects. Shones syndrome diagnosed with echocardiography and. First, there are multiple problems with the left side of the heart, which receives blood from the lungs and pumps it to the body. Shones complex congenital heart disease cove point. Of these four defects, supravalvular mitral membrane svmm is the first to. The valves and passageways are often too small or blocked. Em sua primeira descricao da sindrome, a obstrucao da valvula mitral, apareceu ser a lesao mais critico. Patients with shones syndrome have a poor longterm prognosis, with a perioperative mortality rate of 2427%, often requiring multiple interventions at an early age. A forme fruste of shones anomaly in 65 yearold patient.
Shone syndrome is a collection of eight leftsided obstructive heart lesions. In the complete form, four leftsided defects are present. Malformacoes congenitas cianogenicas linkedin slideshare. Coarctation of the aorta a narrowing or constriction of the aorta, the large vessel that carries blood from the heart to the body tissues. Franck sharko vol 01 le livros baixar livros em pdf. Shones complex also known as shones syndrome, disorder, or anomaly is a rare congenital heart disease consisting of multiple left heart obstructive defects. These affect blood flow to and from the left ventricle, or lower left heart chamber. Shone s syndrome is a rare congenital heart disease described by shone in 1963.